A Case Report of Isolated Vulvar Neurofibroma Radiologically suggested to be a Lipoma
Keywords:
labial mass, neural lesion, NeurofibromaAbstract
Neurofibroma is a benign tumor of peripheral nervous system, which can occur in isolation or be a component of neurofibromatosis type 1. It can occur in any part of the body (except brain and spinal cord) but rarely seen in the female genital areas where, if it ever occurs, the labia are the most frequent site.
We report a case of a 46yr old P0 married woman who presented with a 4 year history of an isolated, slowly growing right sided vulval mass. There were no urogenital or other systemic symptoms. She had no features of neurofibromatosis type 1. She had successful excision biopsy with histologic diagnosis of neurofibroma. The patient had good outcome and is still on follow up.
Neurofibroma of the vulva is rare and may mimic other soft tissue tumours when in solitary occurrence. Excision biopsy, histological diagnosis and keen follow-up are strongly recommended.
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